Histiocitose de células de Langerhans na órbita: Relato de um caso

Histiocitose de células de Langerhans na órbita: Relato de um caso

Autores:

Márcia Cortes,
Luiz Paves,
Deise Mitsuko Nakanami,
Angela Maria Borri Wolosker,
Paulo Góes Manso

ARTIGO ORIGINAL

Arquivos Brasileiros de Oftalmologia

versão impressa ISSN 0004-2749versão On-line ISSN 1678-2925

Arq. Bras. Oftalmol. vol.58 no.6 São Paulo dez. 1995

http://dx.doi.org/10.5935/0004-2749.19950015

SUMMARY

Langerhans' cells histiocytosis (LCH) is a benign disease usually with a good prognosis. We report a case of LCH in a child who presented only orbital affection of sudden onset, axial proptosis, without pain or inflammation. The diagnosis was obtained after imaging followed by incisional biopsy with histopathological examination. Treatment was done inicially with sistemic corticosteroids, introducing chemotherapy later. Clinical course was favorable.

Key words: Langerhans’ cells histiocytosis; Orbit; Proptosis

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