Rabdomiosarcoma orbital

Rabdomiosarcoma orbital


Paulo Góis Manso,
Oswaldo Ignacio Tella Júnior,
Fernando Menezes Braga,
Mauro Rabinovitch,
Italo Suriano


Arquivos Brasileiros de Oftalmologia

versão impressa ISSN 0004-2749versão On-line ISSN 1678-2925

Arq. Bras. Oftalmol. vol.53 no.6 São Paulo nov./dez. 1990


Rhabdomyosarcoma is the most frequent primary orbital malignancy of childhood. Four cases which ages varied from 4 months to 23 years old are described. The typical clinical picture is one of a child with sudden onset and rapid evolution of exophthalmos unilaterally. Biopsy was performed in two cases, exenteration in 1 case and 1 patient was operated on through a left frontal craniotomy. Linfatic metastasis was observed in one case. Comments concerning Chemotherapy and X-ray therapy are made.

Key words: proptosis; embrional rhabdomyosarcoma; hyperemia and chemosis


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