Síndrome de Axenfeld-Rieder associada à maculopatia tipo "Bull's eye"

Síndrome de Axenfeld-Rieder associada à maculopatia tipo "Bull's eye"


Vital P. Costa,
L. Jay Katz,
J. Arch McNamara


Arquivos Brasileiros de Oftalmologia

versão impressa ISSN 0004-2749versão On-line ISSN 1678-2925

Arq. Bras. Oftalmol. vol.58 no.2 São Paulo abr. 1995


The Axenfeld-Rieger syndrome mesodermal dysgenesis represents a spectrum of developmental disorders characterized by abnormalities of the peripheral cornea, íris and anterior chamber angle associated with developmental defects of the teeth and facial banes. Sparse descriptions of fundus abnormalities have been made, but none have been well documented. We report, to our knowledge for the first time, a case of Axenfeld-Rieger syndrome associated with bilateral "bull's eye" maculopathy.

Key words: Axenfeld-Rieger; "bull's eye"; maculopathy; glaucoma


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