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Síndrome de Ehlers-Danlos: descrição de um caso com glaucoma

Síndrome de Ehlers-Danlos: descrição de um caso com glaucoma

Autores:

Sheila Hellen Carvalho Warren,
Roberto Freire Santiago Malta

ARTIGO ORIGINAL

Arquivos Brasileiros de Oftalmologia

versão impressa ISSN 0004-2749versão On-line ISSN 1678-2925

Arq. Bras. Oftalmol. vol.54 no.2 São Paulo mar./abr. 1991

http://dx.doi.org/10.5935/0004-2749.19910032

SUMMARY

The Ehlers-Danlos syndrome comprises a group of alterations of the connective tissue with hereditary character, whose basic alteratians seem to involve the colagenous fibers. Ocular and systemic alterations are described. The authors relate a case of the Ehlers-Danlos syndrome that presented hyperelasticity of the eyelid, myopia, staphyloma, microcornea and glaucoma. The patient was submitted to a trabeculectomy with success.

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